📂 Anatomy
dihydrolipoyl dehydrogenase complex — Definition
dihidrolipoil dehidrogenaz kompleksi / dihydrolipoyl dehydrogenase complex
Dihydrolipoil dehydrogenase complex is a common component of multiple enzyme complexes such as mitochondrial matrikste and pirüvat dehydrogenase, alpha-ketoglutarat dehydrogenase and branch chain alpha-keto acid dehydrogenase. This complex plays a critical role in energy metabolism by dividing the reoxidation of lipoic acid. Deficiency leads to a severe mitochondrial disease characterized by lactic acidosis, neurological disorders and metabolic crises.
Frequently Asked Questions
❓ What is dihidrolipoil dehidrogenaz kompleksi?
dihidrolipoil dehidrogenaz kompleksi; dihydrolipoil dehydrogenase complex is a common component of multiple enzyme complexes such as mitochondrial matrikste and pirüvat dehydrogenase, alpha-ketoglutarat dehydrogenase and branch chain alpha-keto acid dehydrogenase. This complex plays a critical role in energy metabolism by dividing the reoxidation of lipoic acid. Deficiency leads to a severe mitochondrial disease characterized by lactic acidosis, neurological disorders and metabolic crises.
❓ What is dihydrolipoyl dehydrogenase complex in Turkish?
The Turkish equivalent of "dihydrolipoyl dehydrogenase complex" is dihidrolipoil dehidrogenaz kompleksi.
❓ Which medical field is dihidrolipoil dehidrogenaz kompleksi related to?
This term belongs to the Anatomy category.